Research Article

Potter Syndrome: A case study

Konstantinidou P, Chatzifotiou E, Nikolaou A, Moumou G, Karakasi MV, Pavlidis P and Anestakis D*

Published: 08/31/2017 | Volume 1 - Issue 1 | Pages: 063-067


Potter syndrome (PS) is a term used to describe a typical physical appearance, which is the result of dramatically decreased amniotic fluid volume secondary to renal diseases such as bilateral renal agenesis (BRA). Other causes are abstraction of the urinary tract, autosomal recessive polycystic kidney disease (ARPKD), autosomal dominant polycystic kidney disease (ADPKD) and renal hypoplasia. In 1946, Dr Edith Potter characterized this prenatal renal failure/renal agenesis and the resulting physical characteristics of the fetus/infant that result from oligohydramnios as well as the complete absence of amniotic fluid (anhydramnios). Oligohydramnios and anhydramnios can also be due to the result of leakage of amniotic fluid from rupturing of the amniotic membranes. The case reported below, concerns of stillborn boy with potter syndrome.

Read Full Article HTML DOI: 10.29328/journal.jfsr.1001007 Cite this Article


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